High-Power Surgical Laser for Treatment of Oral Manifestations of Mucopolysaccharidosis VI: A Case Report.

Abstract

Mucopolysaccharidosis type VI (MPS VI), a rare metabolic disorder, results from glycosaminoglycan accumulation in tissues, frequently leading to hyperplastic gingival alterations that necessitate comprehensive intervention. An 11-year-old male patient diagnosed with MPS VI required hospitalization due to complications associated with a ventriculoperitoneal shunt (VPS) valve. A dental evaluation identified bone malformation in the maxillomandibular complex accompanied by pronounced gingival hyperplasia. The surgical team performed a gingivoplasty in the operating room under general anesthesia, employing a combined technique involving manual scalpels and a diode laser to excise hyperplastic gingival tissue and cauterize bleeding sites. The patient exhibited an uneventful postoperative recovery, with no hemorrhagic or infectious complications. The diode laser demonstrated safety and efficacy in removing gingival tissue in this patient with MPS VI, facilitating local tissue repair, enhancing the aesthetic and functional profile, and ultimately improving the patient's oral health and quality of life.