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Japanese journal of pediatric nephrology最新文献

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A case of IgA vasculitis, acute glomerulonephritis and Henoch-Schönlein purpura nephritis: successional complications of streptococcal infection IgA血管炎、急性肾小球肾炎和Henoch-Schönlein紫癜性肾炎1例:链球菌感染的连续并发症
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2020.0176
Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku
{"title":"A case of IgA vasculitis, acute glomerulonephritis and Henoch-Schönlein purpura nephritis: successional complications of streptococcal infection","authors":"Minamura Takeichi, Mari Kurokawa, Shinichi Shiona, Y. Kaku","doi":"10.3165/jjpn.cr.2020.0176","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0176","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"1 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"115619013","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
母親に体細胞モザイクや生殖細胞系列モザイク変異を有することが疑われたX連鎖型Alport症候群の男児例 被怀疑母亲体内有体细胞马赛克或生殖细胞系列马赛克变异的X连锁性Alport症候群男孩例子
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2022.0215
Kyoko Suzuki, Takuji Yamada
{"title":"母親に体細胞モザイクや生殖細胞系列モザイク変異を有することが疑われたX連鎖型Alport症候群の男児例","authors":"Kyoko Suzuki, Takuji Yamada","doi":"10.3165/jjpn.cr.2022.0215","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2022.0215","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"57 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125127534","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Efficacy and safety of long-term administration of mycophenolate mofetil after rituximab in patients with refractory nephrotic syndrome 难治性肾病综合征患者利妥昔单抗后长期服用霉酚酸酯的疗效和安全性
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2022.0203
Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa
{"title":"Efficacy and safety of long-term administration of mycophenolate mofetil after rituximab in patients with refractory nephrotic syndrome","authors":"Yooka Nam, R. Hiramoto, S. Shinozuka, S. Matsumoto, H. Eguchi, B. Akikusa","doi":"10.3165/jjpn.oa.2022.0203","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2022.0203","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"180 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"122520358","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
A 3-year-old boy with steroid-resistant nephrotic syndrome who was diagnosed with severe lupus nephritis one year later: a case report 一名患有类固醇抵抗性肾病综合征的三岁男孩,一年后被诊断为严重狼疮肾炎:病例报告
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2021.0202
R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga
{"title":"A 3-year-old boy with steroid-resistant nephrotic syndrome who was diagnosed with severe lupus nephritis one year later: a case report","authors":"R. Ohyama, Mayu Nakagawa, T. Morishita, Shota Endo, Y. Takemasa, Yuta Onuki, Koji Sakuraya, H. Murakami, S. Fujinaga","doi":"10.3165/jjpn.cr.2021.0202","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2021.0202","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"36 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"129682011","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Clinical sequencing for nephrologists 肾科医生的临床测序
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.rv.2021.0002
N. Morisada, Kana Hiromoto
{"title":"Clinical sequencing for nephrologists","authors":"N. Morisada, Kana Hiromoto","doi":"10.3165/jjpn.rv.2021.0002","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2021.0002","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"38 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"133966447","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Assessment of skills in pediatric renal urology procedures among young pediatricians 年轻儿科医生在儿科肾泌尿外科手术中的技能评估
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2021.0197
Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo
{"title":"Assessment of skills in pediatric renal urology procedures among young pediatricians","authors":"Koji Sakuraya, A. Endo, Akina Matsuda, Hiroki Miyano, Hiroaki Gonda, Masahito Saito, Akira Mizutani, Y. Ohtomo","doi":"10.3165/jjpn.oa.2021.0197","DOIUrl":"https://doi.org/10.3165/jjpn.oa.2021.0197","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"200 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128592421","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Characteristic ultrasonic view of the kidneys and pancreas in a neonate with an HNF1B mutation 新生儿HNF1B突变的肾脏和胰腺的特征性超声图像
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.cr.2020.0175
Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda
{"title":"Characteristic ultrasonic view of the kidneys and pancreas in a neonate with an HNF1B mutation","authors":"Y. Inaba, R. Hamada, Ryoko Harada, Junya Hashimoto, Wataru Kubota, Chikako Terano, N. Mikami, H. Hataya, Junpei Kuroda, Uiko Mizuguchi, R. Kakinuma, Masatoshi Kondo, T. Kono, M. Honda","doi":"10.3165/jjpn.cr.2020.0175","DOIUrl":"https://doi.org/10.3165/jjpn.cr.2020.0175","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"21 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"125906632","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Medical safety management at university hospital 高校医院医疗安全管理
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.rv.2022.0003
H. Tsukahara
{"title":"Medical safety management at university hospital","authors":"H. Tsukahara","doi":"10.3165/jjpn.rv.2022.0003","DOIUrl":"https://doi.org/10.3165/jjpn.rv.2022.0003","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"54 1","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"128800685","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
Relapse of nephrotic syndrome during B-cell depletion after single dose of rituximab 单剂量利妥昔单抗后b细胞耗竭期间肾病综合征复发
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.oa.2019.0159
K. Kamei, Mai Sato, Miki Murakoshi, Ryutaro Suzuki, C. Kamae, T. Kanamori, K. Nishi, M. Ogura
We investigated the clinical character of relapses of nephrotic syndrome during B-cell depletion in 137 patients with refractory steroid-dependent nephrotic syndrome who received 375 mg/m 2 of single dose of rituximab. In 440 rituximab treatment, relapses during B-cell deletion were observed 25 times in 19 patients (5.7%). Forty-four percent of them were observed within 14 days after treatment of rituximab. Gender, age of onset of nephrotic syndrome, age at rituximab treatment, renal histology, past histories of steroid resistance showed no difference between patients who relapsed during B-cell depletion and others. Infusion reaction also was not calculated as a risk factor. Two third of patients who relapsed during B-cell depletion could discontinue steroid during B-cell depletion, which showed effectiveness of rituximab. According to the result of this study, we believe that we should maintain doses of steroid as relapse-preventable doses until two weeks after rituximab treatment. Even if patients suffered from relapse during B-cell depletion, rituximab might be effective and their disease character might be pathogenetically same as others. As we could not detect risk factors of relapse during B-cell depletion, prediction is difficult.
我们研究了137例顽固性类固醇依赖性肾病综合征患者在b细胞消耗期间肾病综合征复发的临床特征,这些患者接受了单剂量375 mg/ m2的利妥昔单抗。在440例利妥昔单抗治疗中,19例患者在b细胞缺失期间复发25次(5.7%)。其中44%在利妥昔单抗治疗后14天内观察到。性别、肾病综合征发病年龄、接受利妥昔单抗治疗的年龄、肾脏组织学、既往类固醇抵抗史在b细胞衰竭期间复发的患者和其他患者之间没有差异。输液反应也未作为危险因素计算。三分之二的b细胞耗竭期间复发的患者可以在b细胞耗竭期间停用类固醇,这显示了利妥昔单抗的有效性。根据这项研究的结果,我们认为我们应该维持类固醇的剂量作为预防复发的剂量,直到利妥昔单抗治疗后两周。即使患者在b细胞耗竭过程中复发,利妥昔单抗也可能是有效的,而且他们的疾病特征可能与其他疾病相同。由于我们无法检测到b细胞消耗过程中复发的危险因素,预测是困难的。
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引用次数: 0
森田賞 《臨床研究部門》 辻ゆり佳 森田赏《临床研究部门》辻ゆり佳
Pub Date : 1900-01-01 DOI: 10.3165/jjpn.2022.3007
{"title":"森田賞 《臨床研究部門》 辻ゆり佳","authors":"","doi":"10.3165/jjpn.2022.3007","DOIUrl":"https://doi.org/10.3165/jjpn.2022.3007","url":null,"abstract":"","PeriodicalId":205802,"journal":{"name":"Japanese journal of pediatric nephrology","volume":"249 ","pages":"0"},"PeriodicalIF":0.0,"publicationDate":"1900-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":null,"resultStr":null,"platform":"Semanticscholar","paperid":"120942533","PeriodicalName":null,"FirstCategoryId":null,"ListUrlMain":null,"RegionNum":0,"RegionCategory":"","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":"","EPubDate":null,"PubModel":null,"JCR":null,"JCRName":null,"Score":null,"Total":0}
引用次数: 0
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Japanese journal of pediatric nephrology
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